E70.0Classical phenylketonuria
Code usage status
Primary diagnosis
May be used as the primary diagnosis
Apply only when it matches the confirmed diagnosis and the documented clinical record.
Specificity
Complete code in the classification
Use when the diagnosis matches and no exclusion applies.
- Group E70-E90
- Metabolic disorders
- Official Vietnamese name
- Phenyl-ceton niệu kinh điển
Related E70 codes
E70
Disorders of aromatic amino- acid metabolism
E70.1
Primary diagnosis candidate
Other hyperphenylalanina emias
E70.2
Primary diagnosis candidate
Disorders of tyrosine metabolism
E70.3
Primary diagnosis candidate
Albinism
E70.8
Primary diagnosis candidate
Other disorders of aromatic amino- acid metabolism
E70.9
Primary diagnosis candidate
Disorder of aromatic amino- acid metabolism, unspecified
Clinical record checklist
View coding guide →- Confirm that the code matches the final documented diagnosis.
- Use one primary-diagnosis code and record only relevant additional conditions.
- Review Ministry indicators, inclusions, exclusions and notes.
- Do not infer a diagnosis beyond the clinical record.
2026 regulatory basis
Indicators are taken from columns 24–29 of the classification accompanying Circular 06/2026/TT-BYT, cross-referenced with Decision 1849/QĐ-BYT and Official Dispatch 4059/BYT-BH.