E71.1Other disorders of branched-chain amino-acid metabolism
Code usage status
Primary diagnosis
May be used as the primary diagnosis
Apply only when it matches the confirmed diagnosis and the documented clinical record.
Specificity
Complete code in the classification
Use when the diagnosis matches and no exclusion applies.
- Group E70-E90
- Metabolic disorders
- Official Vietnamese name
- Rối loạn khác của chuyển hóa acid amin chuỗi nhánh
- Additional WHO coding guidance
- Hyperleucine- isoleucinaemia Hypervalinaemia Isovaleric acidaemia Methylmalonic acidaemia Propionic acidaemia
Related E71 codes
E71
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E71.0
Primary diagnosis candidate
Maple-syrup-urine disease
E71.2
Primary diagnosis candidate
Disorder of branched-chain amino-acid metabolism, unspecified
E71.3
Primary diagnosis candidate
Disorders of fatty- acid metabolism
Clinical record checklist
View coding guide →- Confirm that the code matches the final documented diagnosis.
- Use one primary-diagnosis code and record only relevant additional conditions.
- Review Ministry indicators, inclusions, exclusions and notes.
- Do not infer a diagnosis beyond the clinical record.
2026 regulatory basis
Indicators are taken from columns 24–29 of the classification accompanying Circular 06/2026/TT-BYT, cross-referenced with Decision 1849/QĐ-BYT and Official Dispatch 4059/BYT-BH.