Q78.1Polyostotic fibrous dysplasia
Code usage status
Primary diagnosis
May be used as the primary diagnosis
Apply only when it matches the confirmed diagnosis and the documented clinical record.
Specificity
Complete code in the classification
Use when the diagnosis matches and no exclusion applies.
- Official Vietnamese name
- Loạn sản sợi - đa xương
- Additional WHO coding guidance
- Albright(-McCune)(- Sternberg) syndrome
Related Q78 codes
Q78
Other osteochondrodyspla sias
Q78.0
Primary diagnosis candidate
Osteogenesis imperfecta
Q78.2
Primary diagnosis candidate
Osteopetrosis
Q78.3
Primary diagnosis candidate
Progressive diaphyseal dysplasia
Q78.4
Primary diagnosis candidate
Enchondromatosis
Q78.5
Primary diagnosis candidate
Metaphyseal dysplasia
Q78.6
Primary diagnosis candidate
Multiple congenital exostoses
Q78.8
Primary diagnosis candidate
Other specified osteochondrodyspla sias
Q78.9
Primary diagnosis candidate
Osteochondrodyspl asia, unspecified
Clinical record checklist
View coding guide →- Confirm that the code matches the final documented diagnosis.
- Use one primary-diagnosis code and record only relevant additional conditions.
- Review Ministry indicators, inclusions, exclusions and notes.
- Do not infer a diagnosis beyond the clinical record.
2026 regulatory basis
Indicators are taken from columns 24–29 of the classification accompanying Circular 06/2026/TT-BYT, cross-referenced with Decision 1849/QĐ-BYT and Official Dispatch 4059/BYT-BH.