E75.0GM2 gangliosidosis Disease:
Code usage status
Primary diagnosis
May be used as the primary diagnosis
Apply only when it matches the confirmed diagnosis and the documented clinical record.
Specificity
Complete code in the classification
Use when the diagnosis matches and no exclusion applies.
- Group E70-E90
- Metabolic disorders
- Official Vietnamese name
- Bệnh nhiễm gangliosid GM2
- Additional WHO coding guidance
- Sandhoff Tay-Sachs GM2 gangliosidosis: NOS adult juvenile
Related E75 codes
E75
Disorders of sphingolipid metabolism and other lipid storage disorders
E75.1
Primary diagnosis candidate
Other gangliosidosis
E75.2
Primary diagnosis candidate
Other sphingolipidosis
E75.3
Primary diagnosis candidate
Sphingolipidosis, unspecified
E75.4
Primary diagnosis candidate
Neuronal ceroid lipofuscinosis
E75.5
Primary diagnosis candidate
Other lipid storage disorders
E75.6
Primary diagnosis candidate
Lipid storage disorder, unspecified
Clinical record checklist
View coding guide →- Confirm that the code matches the final documented diagnosis.
- Use one primary-diagnosis code and record only relevant additional conditions.
- Review Ministry indicators, inclusions, exclusions and notes.
- Do not infer a diagnosis beyond the clinical record.
2026 regulatory basis
Indicators are taken from columns 24–29 of the classification accompanying Circular 06/2026/TT-BYT, cross-referenced with Decision 1849/QĐ-BYT and Official Dispatch 4059/BYT-BH.