E75Disorders of sphingolipid metabolism and other lipid storage disorders
Code usage status
Primary diagnosis
Select a more specific code
Apply only when it matches the confirmed diagnosis and the documented clinical record.
Specificity
Do not use E75 directly
Use the most specific code supported by the record.
- Group E70-E90
- Metabolic disorders
- Official Vietnamese name
- Rối loạn chuyển hóa sphingolipid và/hoặc rối loạn tích lũy lipid
- Additional WHO coding guidance
- Excl.: mucolipidosis, types I- III (E77.0-E77.1) Refsum disease (G60.1)
Related E75 codes
E75.0
Primary diagnosis candidate
GM2 gangliosidosis Disease:
E75.1
Primary diagnosis candidate
Other gangliosidosis
E75.2
Primary diagnosis candidate
Other sphingolipidosis
E75.3
Primary diagnosis candidate
Sphingolipidosis, unspecified
E75.4
Primary diagnosis candidate
Neuronal ceroid lipofuscinosis
E75.5
Primary diagnosis candidate
Other lipid storage disorders
E75.6
Primary diagnosis candidate
Lipid storage disorder, unspecified
Clinical record checklist
View coding guide →- Confirm that the code matches the final documented diagnosis.
- Use one primary-diagnosis code and record only relevant additional conditions.
- Review Ministry indicators, inclusions, exclusions and notes.
- Do not infer a diagnosis beyond the clinical record.
2026 regulatory basis
Indicators are taken from columns 24–29 of the classification accompanying Circular 06/2026/TT-BYT, cross-referenced with Decision 1849/QĐ-BYT and Official Dispatch 4059/BYT-BH.
